ARVC is an inherited autosomal dominant – the RV myocardium is replaced by fatty & fibro-fatty tissue

Presentation: palpitations, syncope & sudden cardiac death

ECG abnormalities:

• T wave inversion in V1 – 3  in absence of RBBB 
• an epsilon wave (terminal notch in the QRS complex)
• Localised QRS widening in V1-3 (> 110ms)

Management: –

1. Sotalol (the drug of choice)
2. Catheter ablation to prevent ventricular tachycardia
3. Implantable cardioverter-defibrillator